Familial adenomatous polyposis (FAP) is an inherited disorder that typically presents with multiple polyps in the colon. These polyps become cancerous if not monitored in the early stages or if left untreated. For those with a family history of FAP, colonoscopy screenings begin in adolescence and continue throughout adulthood because polyps can arise at an early age. Colon cancer in untreated individuals develops before age 40 years. This topic warrants discussion to aid in the prompt recognition of symptom presentation. This article will address the development of FAP, its presentation, and potential treatment strategies that may be used by nurse practitioners.